Intracranial Extradural Sphenoid Wing Aneurysmal Bone CystExtending into Orbit: A Unique Case

Abstract

Aneurysmal bone cysts (ABC) are benign, expansile, osteolytic and fibro-osseous tumour like lesions commonly seen in children with 80% occurring in the patients less than 20 years of age. The origin of ABC is still debate. We describe a case of 8 year old female with ABC involving right greater wing of sphenoid with intra-orbital extension leading to proptosis. Imaging revealed an expansile multiloculated cystic lesion with fluid-fluid level involving orbital surface of greater wing of sphenoid. The patient underwent right pterional craniotomy and excision. The lesion was multiseptate with dark chocolate coloured fluid and without any dural invasion. Early intervention preserved child’s visual functions. Exact diagnosis by imaging studies  and early surgical resection with complete resection of mass prevents recurrence.